A Case of Incontinentia Pigmenti Associated with Ocular Complications.

Koh, Hyun Kyung; Ahn, Chung Sook

Case Report

Journal of the Korean Ophthalmological Society 1981;22(2):463-467.
Published online February 1, 1981.

A Case of Incontinentia Pigmenti Associated with Ocular Complications.

Hyun Kyung Koh, Chung Sook Ahn

Department of Ophthalmology, College of Medicine, Euha Womans University, Korea.

안증상을 동반한 Incontinentia pigmenti 1예

안정숙(Jung Sook Ahn),고현경(Hyun Kyung Ko)

Abstract

Incontinentia pigmenti is a hereditary anomaly characterized by hyperpigmentation in bizarre irregular patterns of striae, whorls, polyangular flecks, and fountains pray splatters. The dermatosis may be only a part of more generalized disorders which affect with great variability of the teeth, the eyes, the bones or central nervous system, or may be assotiated with other malformations or developmental disturbances. Recently, the authers have been experienced one case of incontinentia pigmenti which is assotiated with ocular complications in a 3 month old female and it was reviewed clinically with literatures.