Treatment of Retinal Detachment occurring in Two Cases of von Hippel-Lindau Syndrome.

Lee, Dong Su; Kim, Yun Young; Kim, Suk Young; Kim, Si Dong

Original Article

Journal of the Korean Ophthalmological Society 2001;42(11):1636-1640.
Published online November 1, 2001.

Treatment of Retinal Detachment occurring in Two Cases of von Hippel-Lindau Syndrome.

Dong Su Lee, Yun Young Kim, Suk Young Kim, Si Dong Kim

Department of Ophthalmology, College of Medicine,Taegu Catholic University.

망막박리가 발생된 von Hippel - Lindau 증후군의 치험 2 예

이동수(Dong Soo Lee),김윤영(Yun Young Kim),김숙영(Suk Young Kim),김시동(Si Dong Kim)

Abstract

PURPOSE
To report two cases of retinal detachment associated with von Hippel-Lindau syndrome, one case of rhegmatogenous retinal detachment combined with mild proliferative vitreoretinopathy and a case of tractional retinal detachment. METHODS: Case reports. Pars plana vitrectomy with membrane peeling and silicone oil tamponade were performed in all cases. Lens aspiration was also performed in one case. RESULTS: Successful retinal reattachment was obtained in all cases. Case 2 developed cataract and secondary glaucoma and was treated with phacoemulsification with posterior chamber lens insertion and YAG laser iridotomy. CONCLUSIONS: In two patients with retinal detachment occurring in von Hippel-Lindau syndrome, we could obtain successful retinal reattachment with stabilized visual acuity after performing pars plana vitrectomy and silicone oil injection.

Key Words: Retinal detachment;Vitrectomy;Von Hippel-Lindau syndrome