Bilateral Serous Retinal Detachment Associated With Alport's Syndrome.

Song, Young Bin; Park, Sung Pyo

doi:2010.51.3.463

J Korean Ophthalmol Soc > Volume 51(3); 2010 > Article

Case Report

Journal of the Korean Ophthalmological Society 2010;51(3):463-468.
DOI: https://doi.org/10.3341/jkos.2010.51.3.463 Published online March 15, 2010.

Bilateral Serous Retinal Detachment Associated With Alport's Syndrome.

Young Bin Song, Sung Pyo Park

Department of Ophthalmology, Kangdong Sacred Heart Hospital, Hallym University College of Medicine, Seoul, Korea. sungpyo@hananet.net

알포트 증후군과 동반된 양안 장액망막박리 1예

송영빈ㆍ박성표

Department of Ophthalmology, Kangdong Sacred Heart Hospital, Hallym University College of Medicine, Seoul, Korea

Abstract

PURPOSE
To report a case of bilateral serous retinal detachment associated with Alport's syndrome that resolved following intensive blood pressure control and electrolyte imbalance correction. CASE SUMMARY: A 50-year-old male patient presented with bilateral lenticonus and bilateral serous retinal detachment. Bilateral serous retinal detachment with retinal flecks characteristic of Alport's syndrome appeared along with the development of chronic renal failure and hypertension. The following kidney biopsy revealed Alport's syndrome. After 14 days, the serous detachment resolved and vision recovered following intensive blood pressure control and electrolyte imbalance correction fundus and FA results were nearly normal. CONCLUSIONS: In this case, bilateral serous retinal detachment in Alport's syndrome resolved with intensive blood pressure control and electrolyte imbalance correction. To the author's knowledge, this is the first case in South Korea with documentation of the onset and resolution of bilateral serous retinal detachment in Alport's syndrome.

Key Words: Alport's syndrome;Serous retinal detachment