A Case of Primary Orbital Hemangioperycytoma.

Lee, Sang Yong; Rho, Joo Heon

Case Report

Journal of the Korean Ophthalmological Society 1998;39(7):1598-1604.
Published online July 1, 1998.

A Case of Primary Orbital Hemangioperycytoma.

Sang Yong Lee, Joo Heon Rho

Department of Ophthalmology, Kosin Medical College, Pusan, Korea.

원발성 안와 혈관주위세포종 1 예

이상용(Sang Yong Lee),노주현(Joo Heon Rho)

Abstract

Hemangiopericytoma is a rare tumor which originate from the soft tissue. The main sites are lower extremity, pelvic retroperitoneum and especially it is rare to occur primarily in the orbit. It is characterized that hemangiopericytoma possesses the potential of malignancy, but prediction of ultimate behavior is difficult because the clinical course often dose not coincide with histopathologic indicators of malignancy. We experienced a case of primary orbital hemagiopericytoma in a 31-yearold man who had complained diplopia and decreased vision, proptosis, downward and outward deviation of right eye. These symptoms had been occured 7 years ago. MRI examination demonstrated a well-defined tissue mass in superomedial extraconal space in the right orbit. We excised the tumor completely and found it was originated from the vessels with immunohistochemical study utilizing CD34 and Factor VIII-R-Ag as diagnostic marker. Also we confirmed the tumor is a hemangiopericytoma in the Gomoris reticulin stain and EM findings. No recurrence occured for more than 12 months after the initial complete excision. So we present our case with a brief review of the lietrature.

Key Words: CD34;EM;Factor VIII-R-Ag;Gomoris reticulin stain;Hemangio pericytoma