Dermatofibrosarcoma in the Orbit: A Case Report.

Lee, Dong Kyu; Kim, Ga Eon; Choi, Won; Yoon, Kyung Chul

doi:2016.57.11.1777

J Korean Ophthalmol Soc > Volume 57(11); 2016 > Article

Case Report

Journal of the Korean Ophthalmological Society 2016;57(11):1777-1780.
DOI: https://doi.org/10.3341/jkos.2016.57.11.1777 Published online November 15, 2016.

Dermatofibrosarcoma in the Orbit: A Case Report.

Dong Kyu Lee, Ga Eon Kim, Won Choi, Kyung Chul Yoon

¹Department of Ophthalmology, Chonnam National University Medical School, Gwangju, Korea. wchoi82@hanmail.net
²Department of Pathology, Chonnam National University Medical School, Gwangju, Korea.

안와에 발생한 피부섬유육종 1예

이동규¹⋅김가언²⋅최 원¹⋅윤경철¹

전남대학교 의과대학 안과학교실¹, 전남대학교 의과대학 병리학교실²

Abstract

PURPOSE
Dermatofibrosarcoma in the orbit is a rare malignant neoplasm. We report an extremely rare case of primary dermatofibrosarcoma in the orbit. CASE SUMMARY: A 66-year-old male presented with a slowly progressing periorbital mass on his left upper eyelid which developed 3 weeks earlier. On physical examinations, a palpable firm mass under the skin was observed at the superomedial aspect of the left upper eyelid. However, there was no surface nodule or demarcated line on the eyelid. An approximately 1.2 × 1 × 1 cm sized well defined and clearly demancated mass was observed on orbital computed tomography. Excisional biopsy was performed under local anesthesia and pathological examination revealed dermatofibrosarcoma. There was no metabolic evidence of regional or distant metastasis based on positron emission tomography-computed tomography. Nine months after surgical excision there was no evidence of local recurrence. CONCLUSIONS: This is the first report in South Korea of dermatofibrosarcoma in the orbit. Dermatofibrosarcoma should be considered following differential diagnosis of a periorbital mass.

Key Words: Dermatofibrosarcoma;Orbital mass