A Case Report of Acute Zonal Occult Outer Retinopathy Showing Acute Idiopathic Blind Spot Enlargement.

Kim, Jong Ho; Kim, Myung Jun; Park, Han Sang

doi:2011.52.3.364

J Korean Ophthalmol Soc > Volume 52(3); 2011 > Article

Case Report

Journal of the Korean Ophthalmological Society 2011;52(3):364-372.
DOI: https://doi.org/10.3341/jkos.2011.52.3.364 Published online March 15, 2011.

A Case Report of Acute Zonal Occult Outer Retinopathy Showing Acute Idiopathic Blind Spot Enlargement.

Jong Ho Kim, Myung Jun Kim, Han Sang Park

Department of Ophthalmology, Kyungpook National University School of Medicine, Daegu, Korea. fhak@dreamwiz.com

급성 특발성 맹점확대증후군 소견을 나타내는 급성 대상잠재성 외망막병증

김종호⋅김명준⋅박한상

Department of Ophthalmology, Kyungpook National University School of Medicine, Daegu, Korea

Abstract

PURPOSE
To present a case of acute zonal occult outer retinopathy (AZOOR) with acute idiopathic blind spot enlargement (AIBSE) investigated using indocyanine green angiography (ICGA), multifocal electroretinography (multifocal ERG) and spectral domain-OCT (SD-OCT). CASE SUMMARY: A healthy 31-year-old female with photopsia and a five-day visual field defect in her left eye showed no abnormal findings in ocular examinations such as slit lamp and fundus examination, fluorescein angiography (FAG), or full field ERG as well as in the systemic neurologic examination. In the late phase of ICGA, there were multiple hypofluorescent spots around the optic disc and scattered through the posterior pole. The patient showed an amplitude decrease of multifocal ERG and the destruction of the boundary between the inner and outer segments of the photoreceptors in the SD-OCT examined in the retinal area corresponding to the visual field defect. The patient was diagnosed with AZOOR and was followed-up without treatment. After three months, no abnormal SD-OCT or visual field test findings were observed and no symptoms remained; however, a slightly depressed response on multifocal ERG was present. CONCLUSIONS: ICGA, multifocal ERG and SD-OCT could be useful methods to detect AZOOR with EBS.

Key Words: Acute idiopathic blind spot enlargement;Acute zonal occult outer retinopathy;Indocyanine green angiography;Multifocal electroretinography;Spectral domain optical coherent tomography