A Case of Neurofibromatosis of the Orbit and Ocular Surface.

Lee, Kwang Hoon; Park, Jin Woo; Yoon, Kyung Chul

doi:2007.48.9.1276

J Korean Ophthalmol Soc > Volume 48(9); 2007 > Article

Case Report

Journal of the Korean Ophthalmological Society 2007;48(9):1276-1280.
DOI: https://doi.org/10.3341/jkos.2007.48.9.1276 Published online September 30, 2007.

A Case of Neurofibromatosis of the Orbit and Ocular Surface.

Kwang Hoon Lee, Jin Woo Park, Kyung Chul Yoon

Department of Ophthalmology, Chonnam University Medical School & Hospital, Gwang-Ju, Korea. kcyoon@chonnam.ac.kr

안와와 안구표면을 동시에 침범한 신경섬유종증 1예

이광훈,박진우,윤경철

Department of Ophthalmology, Chonnam University Medical School & Hospital, Gwang-Ju, Korea

Correspondence: Kyung Chul Yoon, M.D.

Abstract

PURPOSE
To report a case of neurofibromatosis of the orbit and ocular surface. METHODS: A 26-year-old man was admitted complaining of conjunctival mass and exophthalmos. Lisch nodules on the iris were observed in the right eye, and corneal opacity with neovascularization and conjunctival mass were detected in the left eye. Orbital computed tomography revealed diffuse infiltrating facial tumors including the left orbit, suggestive of plexiform neurofibromatosis. RESULTS: We performed evisceration of the left eye and excision of the left orbital mass. Histopathologic examination revealed neurofibroma which was positive for S-100. No recurrence was detected during a 6-month post-operative period.

Key Words: Lisch Nodule;Orbital Neurofibromatosis