Atypical Vogt-Koyanagi-Harada Syndrome in a 7-Year-Old Boy. |
Jaeryung Oh, In Kyung Oh, Kuhl Huh |
Department of Ophthalmology, Korea University College of Medicine, Korea. dumky@unitel.co.kr |
7세 남아에서 발생한 비정형적인 보크트-고야나기-하라다 증후군 |
오재령 ( O Jae Lyeong ) , 오인경 ( O In Gyeong ) , 허걸 ( Heo Geol ) |
|
|
Abstract |
PURPOSE Vogt-Koyanagi-Harada syndrome is more common in adults than in children. We report a atypical case of Vogt-Koyanagi-Harada syndrome like white dot syndromes in a 7-year-old child. METHODS: A 7-year-old child visited with complaints of decreased binocular visual acuity. Under ophthalmologic examination, anterior uveitis and optic neuropathy were found. But there was no other retinal lesion. After high-dose intravenous corticosteroids pulse therapy, yellow pigment lesions like white dot syndromes developed in peripheral retina and enlarged without serous retinal detachment. RESULTS: In 5 months after high-dose intravenous corticosteroids pulse therapy, anterior inflammation was decreased and visual acuity was 0.8 in both eyes. But depigmented retinal lesions were increased and sunset glow occurred. Alopecia and poliosis of hair were found. Human leukocyte antigen typings revealed HLA-DR4 antigen. |
Key Words:
Children;Vogt-Koyanagi-Harada syndrome;White dot syndrome |