Mesectodermal Leiomyosarcoma :A Case Report.

Moon, Seong Heon; Woo, Kyung In; Kim, Yoon Duck; Suh, Yeon Lim

Case Report

Journal of the Korean Ophthalmological Society 2000;41(3):777-783.
Published online March 1, 2000.

Mesectodermal Leiomyosarcoma :A Case Report.

Seong Heon Moon, Kyung In Woo, Yoon Duck Kim, Yeon Lim Suh

¹Department of Ophthalmology, Samsung Medical Center, School of Medicine, Sungkyunkwan University.
²Department of Pathology, School of Medicine, Sungkyunkwan University.

안와에 생긴 중외배엽성 평활근육종 1 례

문성헌(Seong Heon Moon),우경인(Kyung In Woo),김윤덕(Yoon Duck Kim),서연림(Yeon Lim Suh)

Abstract

The mesectodermal leiomyosarcoma of the orbit is extremely rare disease. An 81-year-old woman presented with progressive painless proptosis in her right eye of 1 month duration. Computed tomographic scan of the orbit demonstrated 5-cm size lobulating mass of the right orbit which displaces eyeball anteriorly and bulges out to temporalis portion with severe destruction of lateral orbital wall and intracranial extension. For diagnostic pur-pose, incisional biopsy was performed. Light microscopic examination showed the characteristics of neurogenic tumor. Electron microscopic examination disclosed the features of smooth muscle cells as well as neural differentiation of the tumor, leading to the diagnosis of mesectodermal leiomyosarcoma. To the best of our knowledge, this is the first case of mesectodermal leiomyosar-coma of the orbit in Korea

Key Words: Mesectodermal leiomyosarcoma;Orbital tumor;Proptosis