Moyamoya Disease with Characteristic Funds Findings of Retinal Vascular Insufficiency.

Kim, Yeon Sam; Lee, Ki Sook; Kim, Soon Hyun; Byun, Young Ja

Original Article

Journal of the Korean Ophthalmological Society 1998;39(10):2477-2483.
Published online October 1, 1998.

Moyamoya Disease with Characteristic Funds Findings of Retinal Vascular Insufficiency.

Yeon Sam Kim, Ki Sook Lee, Soon Hyun Kim, Young Ja Byun

¹Department of Ophthalmology, Seoul Adventist Hospital, Seoul, Korea.
²Department of Ophthalmology, College of Medicine, Yonsei University, Seoul, Korea.

안동정맥 혈류장애를 동반한 Moyamoya 병

이기숙(Ki Sook Lee),변영자(Young Ja Byun),김연삼(Yeon Sam Kim),김수현(Soon Hyun Kim)

Abstract

Moyamoya disease is characterized by progressive stenosis of internal carotid artery and shows unique angioraphic findings. Its etiology is still unknown, and theories of immunophysiologic and inflammatory mechanisms remain unproven. These patients show various neurologic symptons by cerebral ischemia, infarction and gemorrhage. and they also show various ophthalmologic symptoms. We experienced that a 21-year-old female who was diagnosed to have moyamoya disease presented with a suddenly developed occipital headache and neurologic deficit. The etiology of her characteristic fundus findings was thought to be retinal vascular insufficiency.

Key Words: Moyamoya disease;Internal carotid artery;Vascular insufficiency