Management of Ectopia Lentis in Children.

Yu, Young Suk; Awh, Jae Yoon; Lee, Jin Hak

Original Article

Journal of the Korean Ophthalmological Society 1999;40(7):1973-1978.
Published online July 1, 1999.

Management of Ectopia Lentis in Children.

Young Suk Yu, Jae Yoon Awh, Jin Hak Lee

Department of Ophthalmology, College of Medicine, Seoul National University, Seoul, Korea.

소아의 선천 수정체탈구의 치료

유영석(Young Suk Yu),오재윤(Jae Yoon Awh),이진악(Jin Hak Lee)

Abstract

To know the causes and visual prognosis of ectopia lentis in children, medical records of 41 patients (82 eyes) were retrospectively analysed.The patients were divided into systemic disease-associated, simple, and familial types according to the causes and directions of lens deviation were compared.Surgical methods, pre-and post-operative corrected vision, and complications were investigated. The mean age at diagnosis was 45/12 years old. The decreased vision (87%) and the presence of family history (7.3%) werethe chief complaints on the first examination. According to the causes, 19patients had Marfan syndrome, 14 simple type, and 8 familial type respectively. The directions of lens deviation in Marfan syndrome were different from in simple and familial types. Surgical management have been per-formed in twenty-six patients (44 eyes) on the average 6years of age, and all but one showed an improvement of postoperative corrected vision. One eye presented a dyscoria as a complication. These results are the first report in Korea about the causes and the visual prognosis of ectopia lentis in children and may give us a reference for further management of these patients.

Key Words: Children;Ectopia lentis;Marfan syndrome;Surgical methods;Visual prognosis