Rhabdomyosarcoma of The Lacrimal Sac in 32-year-old Man.

Woo, Kyung In; Kim, Yoon Duck

Case Report

Journal of the Korean Ophthalmological Society 1996;37(4):702-707.
Published online April 1, 1996.

Rhabdomyosarcoma of The Lacrimal Sac in 32-year-old Man.

Kyung In Woo, Yoon Duck Kim

Department of Ophthalmology, Samsung Medical Center, Seoul, Korea.

32세 남자의 누낭에서 발견된 횡문근육종

우경인(Kyung In Woo),김윤덕(Yoon Duck Kim)

Abstract

A 32-year-old man visited our clinic with complaints of left epiphora and neck masses. A computed tomographic scan demonstrated a well-demarcated homogeneous mass in left lacrimal sac area and a polypoid mass in ethmoidosphenoidal sinuses, and showed multiple lymphadenopathy in neck. Dacryocystectomy and ethmoidosphenoidectomy were performed. Pathologic diagnosis by immunohistochemical study and electron microscopic examination was alveolar type rhabdomyosarcoma. Subsequently, chemotherapy and radiotherapy were done. There was no evidence of recurrence of the tumor in lacrimal sac and paranasal sinus throughout 9 months of follow-up period. The masses in the neck nearly disappeared. Rhabdomyosarcoma in one's thirties is extremely rare and to our knowledge, this patient represents the first case reported to have developed such a tumor in the lacrimal sac. Although rhabdomyosarcoma is very uncommon, there is a rationale for including it in differential diagnosis of a rapidly growing tumor in the lacrimal sac.

Key Words: Lacrimal sac;Paranasal sinus;Rhabdomyosarcoma