A Case of Progressive Inherited Retinal Arteriolar Tortuosity with Spontaneous Retinal Hemorrhage.

Ryou, J H; Park, M G; Yoon, H Y

Case Report

Journal of the Korean Ophthalmological Society 1997;38(2):325-330.
Published online February 1, 1997.

A Case of Progressive Inherited Retinal Arteriolar Tortuosity with Spontaneous Retinal Hemorrhage.

¹Department of Ophthalmology, National Police Hospital, Seou., Korea.
²Department of Ophthalmology, Asan Medical Ceater, Seoul, Korea.

자발성 망막 출혈이 동반된 진행성 유전성 망막세동맥 구불거림

류지한(Ryou J.H),박미경(Park M.G),윤영희(Yoon H.Y)

Abstract

Progressive inherited retinal arteriolar tortuosity is a congenital disorder which is transmitted in an autosomal dominant pattern. Arterioles in the posterior pole are usually affected and the patient become symptomatic only when he develops spontaneous retinal hemorrhage. There are few reports about this over the world. We experienced a case of 23 years old man who presented with progressive inherited retinal arteriolar tortuosity with spontaneous bilateral macular hemorrhages and decreased visual acuity of his right eye. His mother also showed similar retinal arteriolar tortuosity. To our best knowledge, this is the first report in Korea.

Key Words: progressive inherited retinal arteriolar tortuosity;spontaneous retinal hemorrhage