A Case of Congenital Glaucoma Associated with Phakomatosis Pigmentovascularis.

Kim, Yong Yeon; Lee, Soo Jeong; Lee, Tae Soo

Case Report

Journal of the Korean Ophthalmological Society 1997;38(3):413-416.
Published online March 1, 1997.

A Case of Congenital Glaucoma Associated with Phakomatosis Pigmentovascularis.

Yong Yeon Kim, Soo Jeong Lee, Tae Soo Lee

Department of Ophthalmology, Korea University College of Medicine, Seoul, Korea.

색소혈관모반증에 병발한 선천성 녹내장

김용연(Yong Yeon Kim),이수정(Soo Jeong Lee),이태수(Tae Soo Lee)

Abstract

Phakomatosis pigmentovascularis is a developmental syndrome associated with cutaneous hemangioma with melanocytic or epidemal nevi. It was first reported in 1947 by Ota, and can be classified into localized and systemic forms. Melanosis oculi is a common finding in phakomatosis pigmentovascularis, and glaucoma has also been reported. The authors report a case of bilateral congenital glaucoma associated withphakomatosis pigmentovascularis type IIb in a 2-month-old girl who underwent trabeculotomy, followed by successful control of intraocular pressure for the period of 12 months follow-up.

Key Words: Phakomatosis pigmentovascularis, Congenital glaucoma