A Case of Orbital Rhabdomyosarcoma.

Pak, Kyu Hong; Cho, Moon Ja; Chung, San Moon; Beak, Nam Ho

Case Report

Journal of the Korean Ophthalmological Society 1990;31(5):691-695.
Published online May 1, 1990.

A Case of Orbital Rhabdomyosarcoma.

Kyu Hong Pak, Moon Ja Cho, San Moon Chung, Nam Ho Beak

Department of Ophthalmology, Catholic University Medical College, Seoul, Korea.

안와 횡문근육종의 1 예

백남호(Nam Ho Baek),박규홍(Kyu Hong Pak),조문제(Moon Je Cho),정상문(Sang Moon Chung)

Abstract

The orbital rhabdomyosarcoma is the most common primary malignant tumor of the orbit in childhood. It was first described in 1854 by Weber and has been increased possibly due to improvement of diagnostic procedures. A 7-year-old boy with the complaints of proptosis and visual disturbance coincidently had an ocular trauma. Incision and drainage of intraorbital hematoma was performed in the right orbit which was confirmed with orbital CT scan. Microscopic findings showed ovoid and spindle shaped rhabdoblasts, hyperchromatic nuclei, and characteristic cross striation in the cytoplasm of the giant cells. He was diagnosed as embryonal rhabdomyosarcoma. The intraorbital hematoma and surrounding tissue in the right orbit were excised and the right eye was enucleated. He received chemotherapy and radiation therapy.

Key Words: rhabdomyosarcoma;proptosis;hematoma;rhabdoblasts;cross-striation