A Case of Hand-Schuller-Christian Disease with Exophthalmos.

Jun, Yoon Soo; Lee, Won Ryul; Kim, Jae Ho

Case Report

Journal of the Korean Ophthalmological Society 1988;29(1):207-213.
Published online January 1, 1988.

A Case of Hand-Schuller-Christian Disease with Exophthalmos.

Yoon Soo Jun, Won Ryul Lee, Jae Ho Kim

Department of Ophthalmology, Kangnam St, Mary's Hospital, Catholic Medical College, Seoul, Korea.

안구돌출을 동반한 Hand - Schuller - Christian 병

전윤수(Yoon Soo Jun),이원렬(Won Ryul Lee),김재호(Jae Ho Kim)

Abstract

Hand-Schuller-Christian disease, eosinophilic granuloma and Letterer-Siwe disease are classified as histiocytosis-x, on the basis of the underlying proliferation of histiocytes in all three conditions and of their indefinite etiology. The authors experienced a case of Hand-Schuller-Christian disease with exophthalmos. A 17 months old boy was admitted to our Dept. of Ophthalmology because of left exophthalmos since 2 months ago. A biopsy demonstrated that the lesion was Hand-Schuller-Christian disease. The patient was treated with chemotherapy and low dose radiation therapy. We report our experience with this patient along with the review of other papers in this report.