Angioid Streaks of the Retina Associated with Pseudoxanthoma Elasticum.

Kwon, Jang Sool; Kim, Hong Bok; Choi, Ouk

Case Report

Journal of the Korean Ophthalmological Society 1978;19(3):303-307.
Published online March 1, 1978.

Angioid Streaks of the Retina Associated with Pseudoxanthoma Elasticum.

Jang Sool Kwon, Hong Bok Kim, Ouk Choi

Department of Ophthlmology, Yonsei Unirersity College of Medicine, Seoul, Korea.

탄력섬유성위황색종에 합병된 망막색소선조

권장술 , 김홍복 , 최억 ( Jang Sool Kwon , Hong Bok Kim , Ouk Choi )

Abstract

Angioid streaks are a peculiar spoke-like distribution of dark-colored broad lines in the retinaradiating out from the optic nerve in a fashion similiar to the branching of blood vessels. It is thought to be due to breaks in the elastic lamina of Bruch's membrane. Their colour may be reddish-brown. dark-brown, grey or even in parts white. During a ophthalmoscopic examination they may be mistaken for retinal vessels. The lesion, however, lies beneath the retinal and above the choroidal vessels. Angioid streaks are most commonly seen in pseudoxanthoma elasticum, Paget's disease of bone and sickle cell anemia. Angioid streaks with pseudoxanthoma elasticum have been reported in all races and in all decades of life. The peak age lies between 30 and 50. Pseudoxnnthoma elasticum is a dermatologic condition characterized by changes in the elastic tissue of the skin. A 21 year old Korean lady with pseudoxanthoma e!asticum has been found to have angioid streaks in her both fundi.