A Case of Orbital Neuroblastoma.

Koo, Wan Hun; Lee, Dong Jae; Kim, Kyung Woo; Hur, Man Ha

Case Report

Journal of the Korean Ophthalmological Society 1978;19(3):325-331.
Published online March 1, 1978.

A Case of Orbital Neuroblastoma.

Wan Hun Koo, Dong Jae Lee, Kyung Woo Kim, Man Ha Hur

¹Department of Ophthalmology, Maryknoll Hospital, Busan, Korea.
²Department of Pathology, Maryknoll Hospital, Busan, Korea.

안와내 신경아세포종의 (神經芽細胞腫) 1예

허만하(Man Ha Hur),구완헌(Wan Hun Koo),이동재(Dong Jae Lee)

Abstract

Orbital neuroblastoma is the most common childhood metastatic malignant tumor almost always originating from the adrenal medulla; orbital primary origin is very rare. The authors experenced a case of orbital neuroblastoma. The patient was 3 year old Korean female child who was in apparently good health and no abnormalities noted of physical examminations when she developed ecchymosis of right lower lid. About two week later, she quickly developed a growing mass in the right lower orbital soft tissue. The mass was removed and his topathologically diagnosed as neuroblastoma. Radiotherapy was recommended. About 4 months bter, the patient was readmitted because of recurrence of orbital mass 3t the same site. At surgery, tumor was found invading inner and flooe wall of the orbital bone. The patient died of poor course of the disease, about one year after the onset of symptoms. It was suggested that this case was represented metastatic orbital neuroblastoma on histopathological base, but authors were unable to determine the primary site. A brief review of the related literatures is present.