J Korean Ophthalmol Soc > Volume 56(12); 2015 > Article
Journal of the Korean Ophthalmological Society 2015;56(12):1969-1973.
DOI: https://doi.org/10.3341/jkos.2015.56.12.1969    Published online December 15, 2015.
Radius-Maumenee Syndrome Presenting with Ocular Pain and Conjunctival Injection: A Case Report.
Byeong Soo Kang, Eun Ji Lee, Hee Kyung Yang
1Department of Ophthalmology, Seoul National University College of Medicine, Seoul, Korea. eye@snubh.org
2Department of Ophthalmology, Seoul National University Bundang Hospital, Seongnam, Korea.
안통과 충혈을 주소로 내원한 라디우스-마메니 증후군 환자 증례 1예
강병수1⋅이은지1,2⋅양희경1,2
서울대학교 의과대학 안과학교실1, 분당서울대학교병원 안과학교실2
Received: 17 April 2015   • Revised: 16 July 2015   • Accepted: 22 September 2015
Abstract
PURPOSE
Radius-Maumenee syndrome (RMS) is characterized by idiopathic dilated episcleral vessels usually associated with glaucoma. The authors report a case of a 32-year-old Korean male with dilation of the episcleral vessels and glaucoma in both eyes. CASE SUMMARY: A 32-year-old Korean male presented with conjunctival injection and chronic pulsatile ocular pain in both eyes for 11 years. His best corrected visual acuity was 20/20 in both eyes. Slit lamp biomicroscopy showed episcleral venous engorgement in both eyes. Fundus photographs revealed superotemporal and inferotemporal retinal nerve fiber layer defects and Humphrey visual field testing showed superior nasal steps and paracentral scotomas in both eyes. He suffered from chronic eye pain in both eyes although he had applied glaucoma medication and his symptoms had worsened during the past year. Brain magnetic resonance imaging (MRI) and magnetic resonance angiography (MRA) revealed no evidence of carotid cavernous fistula or other orbital lesions. Due to the presence of episcleral venous engorgement, glaucoma and negative tests for other possible diseases, he was diagnosed with RMS. CONCLUSIONS: RMS is an idiopathic disease with episcleral vessel dilation and frequently associated with glaucoma. Its diagnosis is confirmed by eliminating other possible causes of episcleral venous engorgement.
Key Words: Dilated episcleral vein;Open angle glaucoma;Radius-Maumenee syndrome


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